Giant congenital nevocellular nevus and natal teeth.

Congenital nevocellular or nevomelanocytic nevi (CNN) are considered to be hemartomatous lesions of melanocytes apparent at birth(l-3). Though CNN has an incidence of 1% of all newborns, its spectacular variantthe giant or bathing trunk nevus is extremely rare, occuring once in 5,00,000 live births(l). Giant CNN is of devastating consequence due to the cosmetic disfigurement and the great risk for malignant transformation. We report a neonate presenting at birth with giant CNN and natal teeth and the problems in management of such cases.